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DeCS
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Descriptor English:
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Bulbar Palsy, Progressive
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Descriptor Spanish:
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Parálisis Bulbar Progresiva
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Descriptor Portuguese:
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Paralisia Bulbar Progressiva
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Synonyms English:
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Bulbar Palsies
Bulbar Palsies, Progressive
Bulbar Palsy
Bulbar Palsy, Progressive, Of Childhood
Bulbar Paralyses
Bulbar Paralysis
Childhood Progressive Bulbar Palsy
Fazio Londe Disease
Fazio Londe Syndrome
Fazio-Londe Disease
Fazio-Londe Syndrome
Palsies, Bulbar
Palsies, Progressive Bulbar
Palsy, Bulbar
Palsy, Progressive Bulbar
Paralysis, Bulbar
Progressive Bulbar Palsies
Progressive Bulbar Palsy
Progressive Bulbar Palsy of Childhood
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Tree Number:
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C10.574.562.300
C10.668.467.300
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Definition English:
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A motor neuron disease marked by progressive weakness of the muscles innervated by cranial nerves of the lower brain stem. Clinical manifestations include dysarthria, dysphagia, facial weakness, tongue weakness, and fasciculations of the tongue and facial muscles. The adult form of the disease is marked initially by bulbar weakness which progresses to involve motor neurons throughout the neuroaxis. Eventually this condition may become indistinguishable from AMYOTROPHIC LATERAL SCLEROSIS. Fazio-Londe syndrome is an inherited form of this illness which occurs in children and young adults. (Adams et al., Principles of Neurology, 6th ed, p1091; Brain 1992 Dec;115(Pt 6):1889-1900) |
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History Note English:
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2000(1966)
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Allowable Qualifiers English:
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Record Number:
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10433
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Unique Identifier:
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D010244
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Occurrence in VHL:
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Similar:
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DeCS
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